Juvenile xanthogranuloma in neurofibromatosis type 1: prevalence and possible correlation with lymphoproliferative diseases.

Abstract

Neurofibromatosis type 1 (NF1), is a rare genetic disorder that may involve almost every organ system in the body such as cutaneous, ophthalmologic and central and peripheral nervous system.

Cutaneous findings are usually the first sign of the disease. In this study, we investigate the real prevalence of xanthogranulomas juvenile and possible correlation with lymphoproliferative diseases.

PDF (Italiano)